Are there any problems with hearing that occur with EDS?

Hearing impairment and/or sensitivity can occur due to the possibility of hypermobility of the joints between these bones of the middle ear (malleus, incus  and stapes) can create problems with effective sound conduction across the middle ear. This loss of energy in route to the inner ear leads to a mild to moderate conductive hearing loss. Because the inner ear is also responsible for balance, improper function leaves some affected with bouts of dizziness. 

Resource[Amanda Jenner, Lynne Shields, PhD. "EDS Speech and Language Issues."]

The safe and effective way of treating the mild to moderate hearing impairment which can occur in EDS is with hearing aid and necessary additional aids. There is a much more common inherited disorder of hearing know as oloscterosis which can be easily confused with the type of hearing impairment that is seen in EDS. It is vitally important for the ear surgeon to be able to differentiate between the two. As the hearing loss in both is due to abnormality of the sound conduction across the middle ear. The standard treatment for oloscterosis is an operation called, a "stapedectomy". However, do not attempt to undertake a stapedectomy on an EDS patient as it could easily end in disaster with total loss of hearing and a severe disruption of balance.

Resource[M. Hawthorne, FRCS. "Hearing Impairment and EDS."]

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