Classical Type: Management
Gaping skin wounds should be approached with care.
Proper repair of these wounds is necessary to prevent cosmetic
disfigurement. Surgical procedures can be risky, as fragile tissues can unexpectedly tear. Suturing may present problems for the same reason.
The daily use of sunscreen should be used to protect
against excessive sun exposure. One should avoid activities that cause
the joint to lock or overextend. Some patients have responded to
ascorbic acid (Vitamin C) as a treatment to decrease bruising and improve wound healing.
In general, medical intervention is limited to symptomatic therapy but includes:
- prompt surgical assessment in arterial rupture
- delayed removal of sutures
- and surgical repair of frequent articular subluxations
Physicians may also:
- prescribe bracing to stabilize joints
- consult a physical and\or occupational therapist to help patients
strengthen muscles and to teach patients how to properly use and
preserve their joints.
Prior to pregnacy, patients with EDS should have
genetic counseling. Children with EDS should be provided with
information about the disorder, so they can understand why contact
sports and other physically stressful activities should be avoided.
Children should be taught early on that demonstrating the unusual
positions they can maintain due to loose joints should not be done as
this may cause early degeneration of the joints. Family members,
teachers and friends should be provided with information about EDS so
they can accept and assist the child as necessary.