Arterial/intestinal/uterine fragility or rupture commonly arise in Vascular Type EDS. Spontaneous arterial rupture has a peak incidence in the third or
fourth decade of life, but may occur earlier. Midsize arteries are
Arterial rupture is the most common cause of sudden death. Acute
diffuse or localized abdominal or flank pain is a common presentation
of arterial or intestinal rupture.
(For more information about treating
complications of Vascular Type EDS in an emergency, please see the Emergency Physician's Reference Guide.)