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Is Cystic medial necrosis associated with Ehlers-Danlos Syndrome (EDS)? |
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Cystic medial necrosis is associated with EDS as well
as other conditions. This is a degenerative disease of the media of the
aorta and other arteries with
loss of elastic tissue and muscle cells. It is a pathological substrate
for aortic dissection. It may also be manifested by proximal aortic
ectasia or aneurysm. Cystic medial necrosis may occur as an isolated
abnormality or as part of a systemic connective tissue disease such
asĀ Marfans syndrome or Ehlers Danlos syndrome. There is an
increased risk of cystic medial degeneration and aortic or arterial
dissection during pregnancy. (Amersham Health Medcyclopaedia)
www.amershamhealth.com
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