There are other more rare forms of EDS and they include:

• Arthrochalasia Type
  
• Dermatosparaxis Type
  
• Kyphoscoliosis Type
  
• EDS V (X-linked, described in a single family)
• EDS VIII (similar to Classical Type except that it also presents with periodontal friability)
• EDS IX (formerly known as Occipital Horn Syndrome)
• EDS X (seen in one family)

EDS XI (Familial Joint Hypermobility Syndrome) was previously removed from the EDS classification. Its relationship to EDS is not yet defined.