Dermatosparaxis Type: Diagnostic Criteria

The major diagnostic criteria for Dermatosparaxis Type EDS are:

  • Severe skin fragility
  • Sagging, redundant skin

The minor diagnostic criteria for Dermatosparaxis Type EDS are:

  • Soft, doughy skin texture
  • Easy bruising
  • Premature rupture of fetal membranes
  • Large hernias (umbilical, inguinal)